There are six major types of EDS. The different types of EDS are classified according to the
signs and symptoms that are manifested. Each type of EDS is a distinct disorder that “runs
true” in a family. This means that an individual with Vascular Type EDS will not have a child
with Classical Type EDS. The types of EDS include:
Hypermobility (Formerly EDS Type III) where joint hypermobility is the dominant clinical
manifestation. Chronic joint and limb pain is a common complaint among individuals with the Hypermobility
Type.
Classical (Formerly EDS Types I & II) where marked skin hyperextensibility (stretchy) with
widened atrophic scars and joint hypermobility are found.
Vascular (Formerly EDS Type IV) is generally regarded as the most serious form of EDS due to
the possibility of arterial or organ rupture. The skin is usually thin and translucent with veins
being seen through the skin. This is most apparent over the chest and abdomen. There are certain
facial characteristics present in some affected individuals. These manifestations include large eyes,
thin nose, lobeless ears, short stature and thin scalp hair.
Kyphoscoliosis (Formerly EDS Type VI) is characterized by general joint laxity and severe
muscle hypotonia (weak muscle tone) at birth are seen in this type of EDS. The muscular hypotonia
can be very pronounced and leads to delayed gross motor development. Individuals with the
Kyphoscoliosis Type present with scoliosis at birth that is progressive.
Arthrochalasia (Formerly EDS Type VII A&B). Congenital hip dislocation
has been present in all biochemically proven
individuals with this type of EDS. Severe generalized joint
hypermobility with recurrent subluxations are seen in individuals with
this type of EDS.
Dermatosparaxis (Formerly EDS Type VIIC). Individuals with Dermatosparaxis
Type EDS have severe skin fragility and substantial
bruising.
8—iPain Living Magazine